VT0087 – RELEASE THE BOUNDARY!!! AN UNUSUAL CASE REPORT.
VT0087 – RELEASE THE BOUNDARY!!! AN UNUSUAL CASE REPORT.
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Dr. MODHWADIA JAYESH D.
, Dr. SHREYA SHAH, Dr.MEHUL SHAH, DR. APEKSHA KATARIA
Abstract
AIM: TO REPORT A RARE CASE OF UNILATERAL CONGENITAL FIBROSIS OF EXTRA OCULAR MUSCLE, MANAGED WITH SERIES OF SURGERIES. METHOD: WE REPORT AN UNUSUAL CASE OF 20 YRS. OLD MALE, PRESENTED IN OCCULOPLASTY SERVICES OF OUR INSTITUTE WITH COMPLAIN OF DEVIATION OF LEFT EYE SINCE BIRTH. ON DETAILED HISTORY & EXAMINATION, EXOTROPIA >45° WITH ASSOCIATED CO-CONTRACTION ON CONVERGENCE BUT NO PALPEBRAL FISSURE HEIGHT CHANGES.OU BCVA 6/6 MAINTAINED WITH TORTICOLLIS. CASE WAS DIAGNOSED AS CONGENITAL FIBROSIS OF EOM.STEPWISE THREE SURGERIES ARE PERFORMED, INITIALLY LR RECESSION, FOLLOWED BY MR RESECTION WITH TEMPORAL SR-IR FIXATION & FINALLY IR RECESSION WITH SCAR RELEASE. THESE EFFORTS RESULTED IN NEGATIVE FORCED DUCTION TEST & GOOD COSMETIC CORRECTION. CONCLUSION: UNILATERAL CONGENITAL FIBROSIS OF EXTRA OCULAR MUSCLE IS A RARE ENTITY, EFFECTIVELY MANAGED WITH PROPER SEQUENCING OF SURGERIES, BASED ON HISTORY & EXAMINATION.
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