DR. VAIBHAV BHATT

DR. LUTHRA SAURABH, DR.SHRUTANJOY MOHAN DAS, DR. ABHIJAAT CHATURVEDI

Abstract

A 52-year-old female presented with gradual progressive DOV and exotropia OS for 25 years. (BCVA CFCF OS). Fundus OD was normal;Fundus OS showed a temporal optic disc pit(ODP), gross RPE atrophic changes & pigment clumping at the posterior pole and inferior retina OS,confirmed on SW-FAF (optos) as corresponding dense hypoautofluorescent areas. OCT showed optic disc pit with retinoschisis involving outer nuclear & inner nuclear layers, gross photoreceptor loss at the macula, extending to the inferior retina. These findings were consistent with extensive chronic ODP maculopathy OS.

ODP is a rare disorder(2 in 10000). Congenital ODP commonly involve temporal and inferotemporal quadrants of the disc. Approximately 25% to 75% of patients develop serous RD and/or retinoschisis of the central macula. Recent advances in VR surgery have markedly improved the visual prognosis in acute ODP maculopathy. However, delayed diagnosis and treatment can lead to poor visual outcomes.